Journal of Otolaryngology and Ophthalmology of Shandong University ›› 2022, Vol. 36 ›› Issue (5): 58-62.doi: 10.6040/j.issn.1673-3770.0.2021.306

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Keratoconus combined with Kayser-Fleischer ring: a case report and literature review

WANG Chuanyu1,2, MU Guoying1   

  1. 1. Department of Ophthalmology, Shandong Provincial Hospital, Cheeloo College of Medicine, Shandong University, Shandong Provincial Hospital Affiliated to Shandong First Medical University, Jinan 250021, Shandong, China;
    2. Cheeloo College of Medicine, Shandong University, Jinan 250012, Shandong, China
  • Published:2022-09-20

Abstract: Keratoconus(KC)is a disease characterized by corneal thinning and ectasia. Hepatolenticular disease is an inherited disorder that primarily affects hepatic copper deposition with the characteristic ocular sign of Kayser-Fleischer ring(K-F ring). KC is considered to be associated with multiple diseases but not with hepatolenticular degeneration. Here, we present a very rare case of keratoconus with Kayser-Fleischer ring, suggesting that there may be a potential relationship between the two diseases.

Key words: Keratoconus, Kayser-Fleischer ring, Hepatolenticular degeneration, Cross-linking

CLC Number: 

  • R772.23
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