大前庭导水管综合征9例临床分析

山东大学耳鼻喉眼学报

大前庭导水管综合征9例临床分析

何晓峥, 许耀东, 龚坚, 郑亿庆, 区永康, 刘翔, 徐秀娟

中山大学附属第二医院耳鼻咽喉科, 广东广州 510120

收稿日期:2006-03-10 修回日期:1900-01-01 出版日期:2006-06-24 发布日期:2006-06-24
通讯作者: 许耀东

HE Xiao-zheng, XU Yao-dong, GONG Jian, ZHENG Yi-qing, OU Yong-kang, LIUXiang, XU Xiu-juan

Department of Otolaryngology, Second Affiliated Hospital of Sun Yatsen University,

Received:2006-03-10 Revised:1900-01-01 Online:2006-06-24 Published:2006-06-24
Contact: XU Yao-dong

摘要/Abstract

摘要： 目的: 探讨大前庭导水管综合征（LVAS）的诊断、听力学表现及治疗。方法:回顾分析我科2000至2005年9例LVAS的病史、听力学及前庭功能检查、影像学检查及治疗结果。结果:9例均为双耳发病，并呈进行性听力下降，8例纯音测听虽以感音神经性聋为主，但低频段存在一定的气骨导差，保守治疗远期效果不理想。结论:对于儿童不明原因的听力下降，首先应排除先天性疾病，合并其他因素造成的听力下降会增加LVAS诊断的难度。对LVAS进行性听力下降者应尽早选配助听器，并考虑行人工耳蜗植入术。

关键词: 大前庭导水管综合征, 诊断, 耳蜗植入术

Abstract: Objective: To explore the diagnosis, hearing and treatment of large vestibular aqueduct syndrome（LVAS）. Method: A retrospective analysis was conducted on the history, auditory and vestibular function，imaging examination, and treatment in 9 cases from 2000 to 2005. Results: All 9 cases presented bilateral large vestibular aqueduct syndrome, and showed progressive hearing loss. Although sensorineural hearing loss was predominant, conductive hearing loss existed in lowtone frequencies in 8 cases. Longterm results of conservative treatment were not ideal. Conclusions: Hearing loss in children with uncertain reasons should be excluded from congenital diseases. Other factors combined can increase difficulties in diagnosis of LVAS. Hearingaids should be used in patients with progressive hearing loss as early as possible and cochlear implantation should be considered.

Key words: Diagnosis, Cochlear implantation , Large vestibular aqueduct syndrome

何晓峥,许耀东,龚坚, 郑亿庆, 区永康, 刘翔, 徐秀娟 . 大前庭导水管综合征9例临床分析[J]. 山东大学耳鼻喉眼学报, 2006, 20(3): 212-214 .

HE Xiao-zheng, XU Yao-dong, GONG Jian, ZHENG Yi-qing, OU Yong-kang, LIUXiang, XU Xiu-juan . [J]. JOURNAL OF SHANDONG UNIVERSITY (OTOLARYNGOLOGY AND OPHTHALMOLOGY), 2006, 20(3): 212-214 .

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