先天性颈正中裂1例并文献复习

doi:10.6040/j.issn.1673-3770.0.2022.505

摘要/Abstract

摘要： 目的探究先天性颈正中裂(congenital midline cervical cleft, CMCC)的发病特点及胚胎学病因,并讨论其手术治疗方案。方法明确诊断后,全麻行“颈前正中裂切除术+双Z形皮瓣修复术”。回顾总结1例CMCC患者的临床资料并文献复习。结果本例患者术后颈部切口一期愈合,随访1年无复发。结论 CMCC是一种极为罕见的颈部发育畸形,其胚胎成因可能与第一/二鳃弓在中线的闭合不全有关。手术完整切除并一期整复,是首选的治疗手段。

关键词: 先天性畸形, 鳃裂畸形, 颈正中裂, 双 Z-成形术

Abstract: Objective To explore the characteristics, therapy, and embryological etiology of congenital midline cervical cleft(CMCC). Methods After pathological diagnosis revealed a skin fistula, the patient underwent surgical treatment: resection of a contractile, longitudinal neck sinus, skin tag, skin lesion and followed by double Z-plasty. And the clinical data of a case of CMCC was retrospectively reviewed along with a review of related literature. Results The postoperative neck incision of the patient healed in one stage. No evidence of recurrence was found during the 1-year follow-up. Conclusion CMCC is a rare congenital abnormality of the neck. CMCC is thought to occur through a failure of the first or second branchial arch fusion. Double Z-plasty is a common technique for the prevention of contracture and restoration of the anterior contour of the neck.

Key words: Congenital abnormalities, Branchial cleft abnormalities, Midline cervical cleft, Double Z-plasty

中图分类号:

R762

彭雅琪,陈良嗣,许咪咪,黄韵烨,盛晓丽. 先天性颈正中裂1例并文献复习[J]. 山东大学耳鼻喉眼学报, 2024, 38(2): 98-102.

PENG Yaqi, CHEN Liangsi, XU Mimi, HUNAG Yunye, SHENG Xiaoli. Congenital midline cervical cleft: a case report and literature review[J]. Journal of Otolaryngology and Ophthalmology of Shandong University, 2024, 38(2): 98-102.

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