关键词: 鼻肿瘤；横纹肌肉瘤；外科手术

Abstract:

Objective To discuss the clinical character,diagnosis, treatment andprognosis of nasal rhabdomyosarcoma(RMS).   Methods  Integrated with a literaturereview, 12 cases of nasal rhabdomyosarcoma were analyzed retrospectively. The RMS originated from the nasal cavity, in 2 cases, maxillary sinus  in 3 cases, and ethmoid sinus  in 1 case, and 4 infiltrated into the maxillary sinus and ethmoidsinus in 4 cases. The primary site was not clear in 2 cases. 2 cases were treated only by operation, 8 by operation, radiotherapeutics and chemotherapeutics, 2 byradiotherapeutics and chemotherapeutics. 6 cases were treated by a nasal endoscopicsurgical procedure, 4 by lateral rhinotomy, and 5 by neck dissection at the same time. Results The survival rates for 1 and 3 years were 75.0%(9/12) and 33.3%（4/12） respectively. Recurrence was found in 7 cases within 1 year. Among them, 5 accepted  retrieval operation and 2 gave up treatment. Conclusions  The prognosisof RMS was bad, early diagnoses, wide surgical resection and integrated treatment could improve survival rate. Nasal endoscopic surgery could reduce operation trauma and has advantages especially for patients in the early stage.

Key words: Nose neoplasms； Rhabdomyosarcoma； Surgical procedures