Journal of Otolaryngology and Ophthalmology of Shandong University ›› 2024, Vol. 38 ›› Issue (2): 98-102.doi: 10.6040/j.issn.1673-3770.0.2022.505

• Original Article • Previous Articles     Next Articles

Congenital midline cervical cleft: a case report and literature review

PENG Yaqi, CHEN Liangsi, XU Mimi, HUNAG Yunye, SHENG Xiaoli   

  1. Department of Otorhinolaryngology & Head and Neck Surgery, Guangdong Provincial People's Hospital (Guangdong Academy of Medical Sciences), Southern Medical University, Guangzhou 510080, Guangdong, China
  • Online:2024-03-20 Published:2024-03-29

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Abstract: Objective To explore the characteristics, therapy, and embryological etiology of congenital midline cervical cleft(CMCC). Methods After pathological diagnosis revealed a skin fistula, the patient underwent surgical treatment: resection of a contractile, longitudinal neck sinus, skin tag, skin lesion and followed by double Z-plasty. And the clinical data of a case of CMCC was retrospectively reviewed along with a review of related literature. Results The postoperative neck incision of the patient healed in one stage. No evidence of recurrence was found during the 1-year follow-up. Conclusion CMCC is a rare congenital abnormality of the neck. CMCC is thought to occur through a failure of the first or second branchial arch fusion. Double Z-plasty is a common technique for the prevention of contracture and restoration of the anterior contour of the neck.

Key words: Congenital abnormalities, Branchial cleft abnormalities, Midline cervical cleft, Double Z-plasty

CLC Number: 

  • R762
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