Journal of Otolaryngology and Ophthalmology of Shandong University ›› 2022, Vol. 36 ›› Issue (6): 60-65.doi: 10.6040/j.issn.1673-3770.0.2021.396

• 临床研究 • Previous Articles    

Surgical treatment of a cataract complicated by anti-glaucoma surgery in an adult patient with Blau syndrome

SHI Boying, LIANG Hao, LI Yihong, TANG Dongyong   

  1. Department of Ophthalmology, The First Affiliated Hospital of Guangxi Medical University, Nanning 530021, Guangxi, China
  • Published:2022-12-07

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Abstract: Objective To observe the effect of surgical treatment of an adult patient with BLAU syndrome diagnosed in the past 11 years who developed a variety of ocular lesions successively, providing guidance and reference for standardized diagnosis and treatment, and perioperative management. Methods This is a case report of 1 adult BLAU syndrome patient who, in the course of the disease, developed binocular uveitis, binocular secondary angle-closure glaucoma, and binocular concurrent cataract. In 2016 his left eye received a glaucoma valve tube implantation, allograft sclera transplantation, anterior chamber remodeling, and pupil reconstruction. In 2020, phacoemulsification of the left eye combined with intraocular lens implantation and peri-iridectomy were performed. In this paper an analysis and summary of the clinical diagnosis, treatment conception and perioperative management of concurrent cataracts in a patient with Blau syndrome is presented. Results Three and six months after the operation, the patient's visual acuity improved significantly, her intraocular pressure returned to normal, the anterior chamber was deep, the peri-iris incision was smooth, and the intraocular lens was in the right position. Conclusion Ocular lesions of patients with Blau syndrome require early and continuous observation and monitoring. After timely, standardized, and well-considered diagnosis and treatment, patients can maintain enough vision to sustain their quality of life.

Key words: Blau syndrome, Uveitis, Cataract, Glaucoma, Phacoemulsification

CLC Number: 

  • R775.3
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