Blau综合征成年患者抗青光眼手术后并发白内障手术治疗1例并文献复习

doi:10.6040/j.issn.1673-3770.0.2021.396

摘要/Abstract

摘要： 目的观察1例既往确诊Blau综合征11年的成年患者先后出现多种眼部病变后手术治疗的效果,为规范化诊疗、围手术期管理提供思路及参考。方法通过报告1例Blau综合征成年患者病程中先后出现双眼葡萄膜炎、双眼继发性闭角型青光眼、双眼并发性白内障,并分别于2016年左眼行青光眼阀管植入+异体巩膜移植+前房成形+瞳孔再造术、2020年行左眼超声乳化白内障吸除联合人工晶状体植入及虹膜周边切除术的病例,分析和总结Blau综合征患者并发性白内障的临床诊疗思维、围手术期管理等。结果患者术后3个月、6个月复查视力明显提高,眼压正常,前房中深,虹膜周切口通畅,人工晶状体位正。结论 Blau综合征患者的眼部病变需要早期、持续的观察和监测,及时给予规范合理的诊疗后患者可保留足够的视力以保障生活质量。

关键词: Blau综合征, 葡萄膜炎, 白内障, 青光眼, 超声乳化术

Abstract: Objective To observe the effect of surgical treatment of an adult patient with BLAU syndrome diagnosed in the past 11 years who developed a variety of ocular lesions successively, providing guidance and reference for standardized diagnosis and treatment, and perioperative management. Methods This is a case report of 1 adult BLAU syndrome patient who, in the course of the disease, developed binocular uveitis, binocular secondary angle-closure glaucoma, and binocular concurrent cataract. In 2016 his left eye received a glaucoma valve tube implantation, allograft sclera transplantation, anterior chamber remodeling, and pupil reconstruction. In 2020, phacoemulsification of the left eye combined with intraocular lens implantation and peri-iridectomy were performed. In this paper an analysis and summary of the clinical diagnosis, treatment conception and perioperative management of concurrent cataracts in a patient with Blau syndrome is presented. Results Three and six months after the operation, the patient's visual acuity improved significantly, her intraocular pressure returned to normal, the anterior chamber was deep, the peri-iris incision was smooth, and the intraocular lens was in the right position. Conclusion Ocular lesions of patients with Blau syndrome require early and continuous observation and monitoring. After timely, standardized, and well-considered diagnosis and treatment, patients can maintain enough vision to sustain their quality of life.

Key words: Blau syndrome, Uveitis, Cataract, Glaucoma, Phacoemulsification

中图分类号:

R775.3

石博影,梁皓,李一洪,唐东永. Blau综合征成年患者抗青光眼手术后并发白内障手术治疗1例并文献复习[J]. 山东大学耳鼻喉眼学报, 2022, 36(6): 60-65.

SHI Boying, LIANG Hao, LI Yihong, TANG Dongyong. Surgical treatment of a cataract complicated by anti-glaucoma surgery in an adult patient with Blau syndrome[J]. Journal of Otolaryngology and Ophthalmology of Shandong University, 2022, 36(6): 60-65.

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