ISSN 1673-3770 CN 37-1437/R
山东大学耳鼻喉眼学报 ›› 2016, Vol. 30 ›› Issue (3): 77-81.doi: 10.6040/j.issn.1673-3770.0.2016.065
刘悦,赵雪,刘岩,金成勋,魏宁,金春顺,王三春
LIU Yue, ZHAO Xue, LIU Yan, JIN Chengxun, WEI Ning, JIN Chunshun, WANG Sanchun
摘要： 目的 探讨IgG4相关性疾病的临床表现、病理学特征及影像学表现。 方法 分析4例IgG4相关性疾病的临床特征、组织病理学及影像学改变,并查阅相关文献进行总结。 结果 本组4例的平均年龄为55岁,男女比例为3∶1。分别发生于颌下腺2例、眼眶1例、颜面部1例。临床表现无显著特异性,均呈无痛渐进性肿胀。病理学改变为淋巴组织及纤维组织增生,其内有较多浆细胞浸润(IgG4阳性浆细胞>50个/HPF,IgG4阳性浆细胞>IgG阳性浆细胞的40%)。影像学上表现为病变区炎性改变。 结论 IgG4相关性疾病是目前临床较为少见的疾病,发病机制尚不明确。需结合临床表现、血清学检测、病理学特征及影像学表现做出最终诊断,进而行及时准确的治疗。
中图分类号:
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