山东大学耳鼻喉眼学报 ›› 2022, Vol. 36 ›› Issue (1): 1-6.doi: 10.6040/j.issn.1673-3770.0.2021.503

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儿童中耳胆脂瘤诊治进展

杨扬,王晓旭,张杰   

  1. 国家儿童医学中心, 首都医科大学附属北京儿童医院 耳鼻咽喉头颈外科/儿童耳鼻咽喉头颈外科疾病北京市重点实验室, 北京 100045
  • 出版日期:2022-01-10 发布日期:2022-02-22
  • 通讯作者: 张杰. E-mail:stzhangj@263.net
  • 基金资助:
    北京市医院管理中心儿科学科协同发展中心专项(XTYB201828);北京市医院管理中心“登峰”计划专项(DFL20191201)

Progress on diagnosis and treatment of middle ear cholesteatoma in children

YANG Yang, WANG Xiaoxu, ZHANG Jie   

  1. Department of Otorhinolaryngology & Head and Neck Surgery, Beijing Children's Hospital, Capital Medical University, National Center for Children's Health / Beijing Key Laboratory for Pediatric Disease of Otolaryngology, Head & Neck Surgery, Beijing 100045, China
  • Online:2022-01-10 Published:2022-02-22

摘要: 儿童中耳胆脂瘤在患病率、发病机制与临床表现等方面都具有人群的特殊性。其起病隐匿,早期诊治成为临床难点。随着对儿童中耳胆脂瘤认识的提高和普及,临床中对此疾病的关注度明显提高。临床分期的应用及手术治疗的精准性趋于完善,伴有腭裂、特纳综合征、唐氏综合症等特殊人群的中耳胆脂瘤患儿的远期预后管理也得到了重视。

关键词: 儿童, 中耳胆脂瘤, 病理生理, 临床分期, 手术策略

Abstract: Middle ear cholesteatoma in children has population specificity in terms of prevalence, pathogenesis, and clinical manifestations. Due to its gradual onset, early diagnosis and treatment have become difficult clinically. With the improvement and popularization of middle ear cholesteatoma in children, this disease is becoming of increasing interest. The application of clinical staging and the accuracy of surgical treatment have greatly improved. The long-term prognosis management of middle ear cholesteatoma in children with cleft palate, Turner syndrome, Down syndrome, and other special populations has also been given importance.

Key words: Children, Middle ear cholesteatoma, Pathophysiology, Clinical stage, Surgical strategy

中图分类号: 

  • R764.29
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